Case Report: Primary Cardiac Sarcoma in a Young Adult

Savitran Eshwar, Proma Ajoy

Abstract


Abstract:

Primary cardiac sarcoma is an exceptionally rare and aggressive malignancy, representing a small fraction of primary cardiac tumors. This case report presents a detailed account of a 28-year-old female who was diagnosed with primary cardiac sarcoma, highlighting the complexities of its presentation, diagnostic approach, and treatment. The patient, previously in good health, experienced a six-month history of progressive dyspnea and intermittent chest pain. Initial evaluations, including an electrocardiogram and chest X-ray, did not reveal significant abnormalities. However, an echocardiogram identified a mass on the left ventricular free wall, leading to further investigation via cardiac MRI. The MRI findings were consistent with a primary cardiac tumor, specifically angiosarcoma, characterized by a heterogeneous mass with areas of necrosis and infiltration. The diagnosis was confirmed by endomyocardial biopsy. 


The patient underwent surgical intervention, which involved partial resection of the left ventricle to excise the tumor. Post-operatively, she received chemotherapy tailored to the tumor's histological profile, incorporating doxorubicin and ifosfamide. Regular follow-up imaging was scheduled to monitor for recurrence and metastasis. This case underscores the diagnostic challenges associated with primary cardiac sarcomas, given their rarity and the non-specific nature of symptoms. It also emphasizes the importance of a multidisciplinary approach, combining advanced imaging, surgical resection, and adjuvant chemotherapy, to manage this aggressive malignancy effectively. Early detection and comprehensive treatment are crucial for improving prognosis in patients with primary cardiac sarcoma.


Keywords


Primary cardiac sarcoma, angiosarcoma, left ventricular mass, cardiac imaging, multidisciplinary treatment.

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References


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DOI: http://dx.doi.org/10.52155/ijpsat.v47.2.6702

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